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产品目录

重组人MCEE(甲基丙二酰辅酶A异构酶)图片
产品货号:
JN0977
中文名称:
重组人MCEE(甲基丙二酰辅酶A异构酶)
英文名称:
Recombinant Human Methylmalonyl-CoA epimerase
产品规格:
10μg|50μg|500μg|1mg
发货周期:
1~3天
产品价格:
询价
本品由我们的哺乳动物细胞表达系统制备而成,目的基因编码的Gln37-Ala176在C端含有His标签。

MCEE质量控制:>95%(还原性SDS-PAGE)

MCEE制剂:液体

MCEE保存:收到货后请置于-20℃,可保存6个月,避免反复冻融。

关于MCEE
Methylmalonyl-CoA epimerase, mitochondrial(MCEE)is an enzyme which belongs to the glyoxalase I family. It converts (S)-methylmalonyl-CoA to the (R) form, catalyses the following chemical reaction: (R)-methylmalonyl-CoA(S)-methylmalonyl-CoA. It plays an important role in the catabolism of fatty acids with odd-length carbon chains. This protein deficiency is an autosomal recessive inborn error of AA metabolism, involving valine, threonine, isoleucine and methionine. This organic aciduria can appear in the neonatal period with life-threatening metabolic acidosis, hyperammonemia, feeding difficulties, pancytopenia and coma.
相关搜索:重组人MCEE(甲基丙二酰辅酶A异构酶)Recombinant Human Methylmalonyl-CoA epimerase
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